Hereditary fructose intolerance (HFI) is an inborn error of fructose metabolism caused by a deficiency of the enzyme aldolase B. Individuals affected with...

fructose intolerance, a potentially fatal condition in which the liver enzymes that break up fructose are deficient. Hereditary fructose intolerance is...

enterocytes is deficient Hereditary fructose intolerance, a hereditary condition caused by a deficiency of liver enzymes that metabolise fructose This disambiguation...

as in hereditary fructose intolerance. It may be a result of an abnormality in the body's ability to absorb nutrients, as occurs in fructose malabsorption...

cycle or be stored as fatty acids. In hereditary fructose intolerance caused by defects in aldolase B, fructose 1-phosphate accumulates in the liver and...

as the cause of hereditary fructose intolerance (HFI). The generic fructose bisphosphate aldolase enzyme cleaves a 6-carbon fructose sugar into two 3-carbon...

syrup form. Since Emetrol contains fructose it is contraindicated for people with hereditary fructose intolerance (HFI). In diabetes patients, it can...

"Essential fructosuria". Orphanet. Retrieved 11 April 2019. "Fructose Intolerance, Hereditary". rarediseases.org. National Organization for Rare Disorders...

manufactured with either sucrose or glucose. Hereditary fructose intolerance Inverted sugar syrup "Fructose". m-w.com. Merriam-Webster. Archived from the...

aldolase B cause hereditary fructose intolerance. The metabolism of free fructose in liver exploits the ability of aldolase B to use fructose 1-phosphate as...

hypersensitivity, and reactive hypoglycemia. Stomach bypass surgery or hereditary fructose intolerance are believed to be causes, albeit uncommon, of reactive hypoglycemia...

Hemolytic anemia Polycystic liver disease Sickle cell disease Hereditary fructose intolerance Hunter syndrome (spleen affected) Zellweger's syndrome Carnitine...

individuals with hereditary fructose intolerance or fructose malabsorption, who have been advised to avoid ingredients that contain fructose. While individuals...

Other errors in fructose metabolism have greater clinical significance. Hereditary fructose intolerance, or the presence of fructose in the blood (fructosemia)...

Cystinosis Galactosemia Glycogen storage disease (type I) Hereditary fructose intolerance Lowe syndrome Tyrosinemia Wilson's disease Acquired disorders...

and fructose which are bonded together. A more familiar name is table, beet, or cane sugar. It was believed that most cases of sucrose intolerance were...

tyrosinemia (type I), galactosemia, glycogen storage diseases, and hereditary fructose intolerance. Two forms, Dent's disease and Lowe syndrome, are X linked...

Conditions that can present similarly include galactosaemia, hereditary fructose intolerance, cystic fibrosis, and biliary atresia. Neonatal jaundice Pediatric...

Acromegaly Shock Galactosemia Several glycogen storage diseases Obesity Convulsions Ectopic hormone production from tumors Hereditary fructose intolerance...

sorbitol. Patients who are allergic to peanut, soya or with rare hereditary fructose intolerance should not take this medicine. It is also contraindicated in...

and therapeutic contexts. (1) Metabolic Disorders Hereditary Fructose Intolerance (HFI) Fructose 1,6-Bisphosphate Deficiency Metabolic Syndrome and Obesity...

Additional contraindications for the children's formulation are hereditary fructose intolerance, glucose-galactose malabsorption and saccharase deficiency...

dietary fructose. Inactivation of the hepatic fructokinase results in asymptomatic fructosuria.[citation needed] Hereditary fructose intolerance (HFI) results...

congenital adrenal hyperplasia, with RE Siebenmann (1957) hereditary fructose intolerance, with R. Froesh, A. Labhart et al. (1957) pseudo-vitamin D...

stores are normal. Acute Hypoglycemia Fructose 1-Phosphate Aldolase Deficiency (Hereditary fructose intolerance). There are two types of glycogen storage...

deafness Hereditary elliptocytosis Hereditary fibrinogen Aα-Chain amyloidosis Hereditary fructose intolerance Hereditary hearing disorder Hereditary hearing...

HFI may refer to: Hereditary fructose intolerance, a metabolic deficiency HFI Flooring Inc, a Canadian company Hamfest India, an amateur radio convention...

hypoglycemia type 7 Fasting Fluorodeoxyglucose Fructose intolerance Fructose-1,6-diphosphatase deficiency Fructose-1-phosphate aldolase deficiency Functioning...

Hereditary fructose intolerance 271.3 Intestinal disaccharidase deficiencies and disaccharide malabsorption Lactose intolerance Glucose intolerance 271...

syndrome Fructose intolerance Fructose-1,6-bisphosphatase deficiency Fructose-1-phosphate aldolase deficiency, heredita Fructosemia, hereditary Fructosuria...