4-alpha-glucan-branching enzyme, also known as brancher enzyme or glycogen-branching enzyme is an enzyme that in humans is encoded by the GBE1 gene. Glycogen branching...

Glycogen-branching enzyme deficiency (GBED) is an inheritable glycogen storage disease affecting American Quarter Horses and American Paint Horses. It...

which causes a defect in the glycogen branching enzyme. Therefore, glycogen is not made properly, and abnormal glycogen molecules accumulate in cells;...

glycogen-branching enzyme deficiency. This condition is caused by a mutation of the GBE1 gene responsible for producing the glycogen branching enzyme...

the interior of the glycogen molecule. The branching enzyme can act upon only a branch having at least 11 residues, and the enzyme may transfer to the...

non-reducing end of the glycogen chain, forming more α(1→4) bonds in the process. Branches are made by glycogen branching enzyme (also known as...

Valberg, Stephanie; James R Mickelson. "Glycogen Branching Enzyme Deficiency (GBED) in Horses". Glycogen Branching Enzyme Deficiency (GBED). University of Minnsesota...

carbohydrates metabolism. Glycogen storage diseases are deficiencies of enzymes or transport proteins which impair glycogen synthesis, glycogen degradation or glycolysis...

The glycogen debranching enzyme, in humans, is the protein encoded by the gene AGL. This enzyme is essential for the breakdown of glycogen, which serves...

breed's Glycogen branching enzyme (GBE1) can cause both a perinatal hypoglycemic collapse and a late-juvenile-onset neuromuscular degeneration in glycogen storage...

A glycogen storage disease (GSD, also glycogenosis and dextrinosis) is a metabolic disorder caused by a deficiency of an enzyme or transport protein affecting...

sequential removal of glucose monomers via phosphorolysis, by the enzyme glycogen phosphorylase. In the muscles, glycogenolysis begins due to the binding...

for glycogen branching enzyme, also called 1,4-alpha-glucan-branching enzyme. The GBE1 gene provides instructions for making the glycogen branching enzyme...

Glycogen phosphorylase is one of the phosphorylase enzymes (EC 2.4.1.1). Glycogen phosphorylase catalyzes the rate-limiting step in glycogenolysis in...

Energy Genome Biology and Evolution, a scientific journal Glycogen branching enzyme, an enzyme The general balance equation, a simplified mass balance relation...

produced after hydrolysis of glycogen. Without glycogen debranching enzymes to further convert these branched glycogen polymers to glucose, limit dextrinosis...

Quarter Horses and Appaloosas), malignant hyperthermia (MH) and glycogen branching enzyme deficiency (GBED). The influence of Thoroughbred breeding puts...

breakdown of glycogen to glucose-1-phosphate for use in muscle. The enzyme removes 1,4 glycosyl residues from the outer branches of glycogen and adds inorganic...

intermediate and highly branched maltodextrins produced from gelatinized starches with various microbial glycogen branching enzymes". Carbohydrate Polymers...

extensively branched and compact than starch. Glycogen is a polymer of α(1→4) glycosidic bonds linked with α(1→6)-linked branches. Glycogen is found in...

up") Equine polysaccharide storage myopathy (EPSM) or (PSSM) Glycogen Branching Enzyme Deficiency (GBED) Hypocalcemia Hyperkalemic periodic paralysis...

extract different glycolytic enzymes from muscle tissue, and combine them to artificially create the pathway from glycogen to lactic acid. In one paper...

the branching enzyme in mycobacteria makes shorter branches compared to glycogen synthesis. For organisms that can utilize both classic glycogen synthesis...

Isoamylase (EC 3.2.1.68, debranching enzyme, glycogen α-1,6-glucanohydrolase) is an enzyme with systematic name glycogen 6-α-D-glucanohydrolase. It catalyses...

acids and glycogen. The metabolism of glycogen is controlled by activity of phosphorylase, the enzyme that breaks down glycogen, and glycogen synthase...

an enzyme involved in converting glucose to glycogen. It acts as a primer, by polymerizing the first few glucose molecules, after which other enzymes take...

core protein Glycogenin, surrounded by branches of glucose units, linked together. The branching of glycogen increases its solubility, and allows for...

and the branched amylopectin. Depending on the plant, starch generally contains 20 to 25% amylose and 75 to 80% amylopectin by weight. Glycogen, the energy...

(glucose synthesis) and glycogenesis (glycogen synthesis) in the liver and glycogenolysis (breakdown of glycogen) in skeletal muscle. It also increases...

to produce glucose 6-phosphate. Glycogen can be converted into glucose 6-phosphate as well with the help of glycogen phosphorylase. During energy metabolism...