Carbamoyl phosphate synthetase catalyzes the ATP-dependent synthesis of carbamoyl phosphate from glutamine (EC 6.3.5.5) or ammonia (EC 6.3.4.16) and bicarbonate...

Carbamoyl phosphate synthetase III (CPS III) is one of the three isoforms of the carbamoyl phosphate synthetase, an enzyme that catalyzes the active production...

Carbamoyl phosphate synthetase (glutamine-hydrolysing) (EC 6.3.5.5) is an enzyme that catalyzes the reactions that produce carbamoyl phosphate in the cytosol...

to form glutamine: Glutamate + ATP + NH3 → Glutamine + ADP + phosphate Glutamine synthetase uses ammonia produced by nitrate reduction, amino acid degradation...

CPS3 may refer to: CP System III, an arcade system board Carbamoyl phosphate synthetase III, an enzyme Parry Sound (Portage Lake) Water Aerodrome, Canadian...

converted into carbamoyl phosphate through the investment of two ATP molecules. This step is facilitated by carbamoyl phosphate synthetase I. The second...

involves the enzyme carbamoyl phosphate synthase combining glutamine with CO2 in an ATP dependent reaction to form carbamoyl phosphate. Aspartate carbamoyltransferase...

lysine residues of proteins. SIRT5 deacetylases and regulates carbamoyl phosphate synthetase (CPS1), the rate-limiting and initiating step of the urea cycle...

deficiences in the enzymes carbamoyl phosphate synthetase I, ornithine transcarbamylase, or argininosuccinic acid synthetase. Uncontrolled, this causes...

ER (August 1976). "DON, CONV and DONV-II. Inhibition of L-'asparagine synthetase in vivo". Biochemical Pharmacology. 25 (16): 1851–1858. doi:10.1016/0006-2952(76)90189-1...

kinase EC 2.7.2.4: aspartate kinase EC 2.7.2.5: Now EC 6.3.4.16, carbamoyl-phosphate synthase (ammonia) EC 2.7.2.6: formate kinase EC 2.7.2.7: butyrate...

syndrome Caratolo–Cilio–Pessagno syndrome Carbamoyl phosphate synthetase deficiency Carbamoyl phosphate synthetase I deficiency Carbohydrate deficient glycoprotein...

in the bloodstream. Ammonia is converted to carbamoyl phosphate by the enzyme carbamoyl phosphate synthetase, and then enters the urea cycle to be either...

259.300 – argininosuccinate synthase MeSH D08.811.464.259.350 – carbamoyl-phosphate synthase (ammonia) MeSH D08.811.464.259.400 – carbon-nitrogen ligases...

the puerperium. Cases have been described in carbamoyl phosphate synthetase 1, argino-succinate synthetase and ornithine carbamoyltransferase deficiency...

mitochondrial enzymes involved in the urea cycle (such as ammonia-dependent-carbamoyl-phosphate synthase or CPS1), and inhibits its mechanism of action. The combination...

Capillary malformation-arteriovenous malformation; 608354; RASA1 Carbamoyl phosphate synthetase I deficiency; 237300; CPS1 Carbohydrate-deficient glycoprotein...

320.565.066.210.490 – Hartnup disease MeSH C16.320.565.066.275 – carbamoyl-phosphate synthase I deficiency disease MeSH C16.320.565.066.340 – citrullinemia...

452.100.100.050 – abetalipoproteinemia MeSH C18.452.100.100.162 – carbamoyl-phosphate synthase I deficiency disease MeSH C18.452.100.100.175 – citrullinemia...