• Thumbnail for Carnitine palmitoyltransferase I
    Carnitine palmitoyltransferase I (CPT1) also known as carnitine acyltransferase I, CPTI, CAT1, CoA:carnitine acyl transferase (CCAT), or palmitoylCoA transferase...
    19 KB (2,459 words) - 00:34, 9 April 2024
  • Thumbnail for Carnitine palmitoyltransferase I deficiency
    Carnitine palmitoyltransferase I deficiency is a rare metabolic disorder that prevents the body from converting certain fats called long-chain fatty acids(LCFA)...
    7 KB (597 words) - 14:52, 27 October 2023
  • Thumbnail for Carnitine palmitoyltransferase II deficiency
    Carnitine palmitoyltransferase II deficiency, sometimes shortened to CPT-II or CPT2, is an autosomal recessively inherited genetic metabolic disorder characterized...
    26 KB (3,166 words) - 14:52, 27 October 2023
  • Thumbnail for Carnitine palmitoyltransferase II
    Carnitine O-palmitoyltransferase 2, mitochondrial is an enzyme that in humans is encoded by the CPT2 gene. Carnitine palmitoyltransferase II precursor...
    9 KB (1,034 words) - 23:07, 18 January 2024
  • Thumbnail for Carnitine O-palmitoyltransferase
    Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme (EC 2.3.1.21) involved in the metabolism...
    2 KB (151 words) - 07:15, 20 October 2022
  • Thumbnail for Carnitine
    acetylcarnitine ester and being transported by carnitine palmitoyltransferase I and carnitine palmitoyltransferase II. Carnitine also plays a role in stabilizing acetyl-CoA...
    30 KB (3,278 words) - 20:35, 26 April 2024
  • Thumbnail for CROT (gene)
    "Structural model of a malonyl-CoA-binding site of carnitine octanoyltransferase and carnitine palmitoyltransferase I: mutational analysis of a malonyl-CoA affinity...
    4 KB (493 words) - 14:06, 13 October 2022
  • Thumbnail for Inborn error of lipid metabolism
    Carnitine palmitoyltransferase I deficiency (CPT) - Carnitine palmitoyltransferase I Carnitine palmitoyltransferase II deficiency (CPT) - Carnitine palmitoyltransferase...
    4 KB (356 words) - 21:16, 7 December 2020
  • dextrorotatory (R)-(+)- enantiomer, is an irreversible inhibitor of carnitine palmitoyltransferase-1 (CPT-1; EC 2.3.1.21) on the inner face of the outer mitochondrial...
    17 KB (1,783 words) - 07:25, 22 April 2024
  • Thumbnail for Glucagon
    (downstream of glycolysis) and an allosteric inhibitor of Carnitine palmitoyltransferase I (CPT1), a mitochondrial enzyme important for bringing fatty...
    24 KB (2,820 words) - 02:59, 22 November 2023
  • Thumbnail for Hepatomegaly
    intolerance Hunter syndrome (Spleen affected) Zellweger's syndrome Carnitine palmitoyltransferase I deficiency Granulomatous: Sarcoidosis The mechanism of hepatomegaly...
    14 KB (1,162 words) - 00:28, 11 December 2023
  • Thumbnail for Rhabdomyolysis
    storage diseases VIII, IX, X and XI Lipid metabolism defects: carnitine palmitoyltransferase I and II deficiency, deficiency of subtypes of acyl CoA dehydrogenase...
    49 KB (4,816 words) - 02:56, 18 January 2024
  • carnitine by carnitine palmitoyltransferase I, located on the cytosolic faces of the outer and inner mitochondrial membranes. Acyl-carnitine is shuttled inside...
    32 KB (3,362 words) - 01:01, 15 April 2024
  • Carbohydrate-deficient glycoprotein syndrome type 1b Carnitine palmitoyltransferase I deficiency Carnitine-acylcarnitine translocase deficiency Chloramphenicol...
    21 KB (1,265 words) - 01:46, 22 December 2023
  • Thumbnail for Carnitine-acylcarnitine translocase deficiency
    [citation needed] Primary carnitine deficiency Carnitine palmitoyltransferase I deficiency Carnitine palmitoyltransferase II deficiency Reference, Genetics...
    5 KB (398 words) - 13:42, 14 September 2023
  • modeling Carnitine palmitoyltransferase I (CPT1A, CPT1, CPT1-L, L-CPT1), a mitochondrial enzyme responsible for the formation of acyl carnitines Carboxypeptidase...
    3 KB (309 words) - 05:20, 23 April 2024
  • Thumbnail for Ketogenesis
    malonyl-CoA from acetyl-CoA. Malonyl-CoA reduces the activity of carnitine palmitoyltransferase I, an enzyme that brings fatty acids into the mitochondria for...
    19 KB (2,337 words) - 21:19, 6 March 2024
  • Thumbnail for Insulin
    Insulin (redirect from Iletin i (beef-pork))
    shunted into lipogenesis and that allosterically inhibits of carnitine palmitoyltransferase I (CPT1), a mitochondrial enzyme necessary for the translocation...
    121 KB (13,799 words) - 14:41, 17 April 2024
  • Thumbnail for Meldonium
    co-A is then exchanged with carnitine (via the enzyme carnitine palmitoyltransferase I) to produce a fatty acid-carnitine complex. This complex is then...
    58 KB (4,893 words) - 21:29, 10 March 2024
  • CAT I may refer to: Instrument landing system#ILS categories Chloramphenicol O-acetyltransferase I, an enzyme Carnitine O-palmitoyltransferase I, another...
    327 bytes (69 words) - 15:29, 11 January 2021
  • mitochondrion the carnitine shuttle is used: Acyl-CoA is transferred to the hydroxyl group of carnitine by carnitine palmitoyltransferase I, located on the...
    50 KB (5,569 words) - 21:52, 31 March 2024
  • Thumbnail for Glibenclamide
    McGarry JD (July 1994). "More direct evidence for a malonyl-CoA-carnitine palmitoyltransferase I interaction as a key event in pancreatic beta-cell signaling"...
    14 KB (1,066 words) - 06:45, 2 March 2024
  • mitochondria, it must react with carnitine in order to be transported across: Palmitoyl-CoA + Carnitine ⇌ Palmitoyl-Carnitine + CoA-SH This transesterification...
    7 KB (600 words) - 14:58, 27 March 2024
  • conditions including glutaric aciduria type 1 in the Oji-Cree and carnitine palmitoyltransferase I deficiency in Hutterites; these screening programs were aimed...
    3 KB (326 words) - 19:10, 9 May 2023
  • deficiency) Phosphoglycerate kinase deficiency Carnitine palmitoyltransferase I deficiency Carnitine palmitoyltransferase II deficiency Medium-chain acyl-coenzyme...
    9 KB (899 words) - 01:15, 30 January 2023
  • conjugated to carnitine by carnitine acyltransferase I (palmitoyltransferase) I located on the outer mitochondrial membrane Acyl carnitine is shuttled inside...
    6 KB (685 words) - 16:38, 10 February 2023
  • carnitine deficiency 277.85 Disorders of fatty acid oxidation metabolism Carnitine palmitoyltransferase I deficiency Carnitine palmitoyltransferase II...
    16 KB (1,399 words) - 17:41, 9 February 2024
  • Thumbnail for Chromosome 11
    Cleavage and polyadenylation specificity factor subunit 7 CPT1A: carnitine palmitoyltransferase 1A (liver) CREBZF encoding protein CREB/ATF bZIP transcription...
    28 KB (1,930 words) - 22:58, 28 March 2024
  • syndrome Carnitine palmitoyl transferase deficiency Carnitine palmitoyltransferase I deficiency Carnitine palmitoyltransferase II deficiency Carnitine transporter...
    40 KB (3,643 words) - 13:46, 22 March 2024
  • Thumbnail for Palmitoylcarnitine
    mitochondria via the carnitine-acylcarnitine translocase. Once inside the inner mitochondrial membrane, the same Carnitine O-palmitoyltransferase family is then...
    6 KB (599 words) - 05:24, 3 January 2024